PDB entry 1fns

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HEADER    IMMUNE SYSTEM                           23-AUG-00   1FNS              
TITLE     CRYSTAL STRUCTURE OF THE VON WILLEBRAND FACTOR (VWF) A1               
TITLE    2 DOMAIN I546V MUTANT IN COMPLEX WITH THE FUNCTION BLOCKING            
TITLE    3 FAB NMC4                                                             
COMPND    MOL_ID: 1;                                                            
COMPND   2 MOLECULE: IMMUNOGLOBULIN NMC-4 IGG1;                                 
COMPND   3 CHAIN: L;                                                            
COMPND   4 FRAGMENT: FAB FRAGMENT, LIGHT CHAIN;                                 
COMPND   5 MOL_ID: 2;                                                           
COMPND   6 MOLECULE: IMMUNOGLOBULIN NMC-4 IGG1;                                 
COMPND   7 CHAIN: H;                                                            
COMPND   8 FRAGMENT: FAB FRAGMENT, HEAVY CHAIN;                                 
COMPND   9 MOL_ID: 3;                                                           
COMPND  10 MOLECULE: VON WILLEBRAND FACTOR;                                     
COMPND  11 CHAIN: A;                                                            
COMPND  12 FRAGMENT: A1 DOMAIN RESIDUES 507 - 702, OR GLYCOPROTEIN              
COMPND  13 IBA (A\:ALPHA) BINDING DOMAIN;                                       
COMPND  14 ENGINEERED: YES                                                      
SOURCE    MOL_ID: 1;                                                            
SOURCE   2 ORGANISM_SCIENTIFIC: MUS MUSCULUS;                                   
SOURCE   3 ORGANISM_COMMON: MOUSE;                                              
SOURCE   4 CELL: HYBRIDOMA CELLS, MOPC21 CELLS;                                 
SOURCE   5 MOL_ID: 2;                                                           
SOURCE   6 ORGANISM_SCIENTIFIC: MUS MUSCULUS;                                   
SOURCE   7 ORGANISM_COMMON: MOUSE;                                              
SOURCE   8 CELL: HYBRIDOMA CELLS, MOPC21 CELLS;                                 
SOURCE   9 MOL_ID: 3;                                                           
SOURCE  10 ORGANISM_SCIENTIFIC: HOMO SAPIENS;                                   
SOURCE  11 ORGANISM_COMMON: HUMAN;                                              
SOURCE  12 EXPRESSION_SYSTEM: ESCHERICHIA COLI;                                 
SOURCE  13 EXPRESSION_SYSTEM_COMMON: BACTERIA;                                  
SOURCE  14 EXPRESSION_SYSTEM_VECTOR_TYPE: T7 PROMOTER;                          
SOURCE  15 EXPRESSION_SYSTEM_PLASMID: PET8C                                     
KEYWDS    VON WILLEBRAND FACTOR, GLYCOPROTEIN IBA (A:ALPHA) BINDING,            
KEYWDS   2 COMPLEX (WILLEBRAND/IMMUNOGLOBULIN), BLOOD COAGULATION TYPE          
KEYWDS   3 2B VON WILLEBRAND DISEASE                                            
EXPDTA    X-RAY DIFFRACTION                                                     
AUTHOR    K.I.VARUGHESE                                                         
REVDAT   3   22-MAY-07 1FNS    1       SOURCE DBREF  SEQRES REMARK              
REVDAT   3 2                   1       MASTER                                   
REVDAT   2   01-APR-03 1FNS    1       JRNL                                     
REVDAT   1   18-OCT-00 1FNS    0                                                
JRNL        AUTH   R.CELIKEL,Z.M.RUGGERI,K.I.VARUGHESE                          
JRNL        TITL   VON WILLEBRAND FACTOR CONFORMATION AND ADHESIVE              
JRNL        TITL 2 FUNCTION IS MODULATED BY AN INTERNALIZED WATER               
JRNL        TITL 3 MOLECULE.                                                    
JRNL        REF    NAT.STRUCT.BIOL.              V.   7   881 2000              
JRNL        REFN   ASTM NSBIEW  US ISSN 1072-8368                               
REMARK   1                                                                      
REMARK   1 REFERENCE 1                                                          
REMARK   1  AUTH   R.CELIKEL,K.I.VARUGHESE,MADHUSUDAN,A.YOSHIOKA,               
REMARK   1  AUTH 2 J.WARE,Z.M.RUGGERI                                           
REMARK   1  TITL   CRYSTAL STRUCTURE OF THE VON WILLEBRAND FACTOR A1            
REMARK   1  TITL 2 D DOMAIN IN COMPLEX WITH THE FUNCTION BLOCKING               
REMARK   1  TITL 3 NMC-4 DOMAIN IN COMPLEX WITH THE FUNCTION BLOCKING           
REMARK   1  TITL 4 NMC-4 FAB                                                    
REMARK   1  REF    NAT.STRUCT.BIOL.              V.   5   189 1998              
REMARK   1  REFN   ASTM NSBIEW  US ISSN 1072-8368                               
REMARK   2                                                                      
REMARK   2 RESOLUTION. 2.00 ANGSTROMS.                                          
REMARK   3                                                                      
REMARK   3 REFINEMENT.                                                          
REMARK   3   PROGRAM     : CNS 0.4                                              
REMARK   3   AUTHORS     : BRUNGER,ADAMS,CLORE,DELANO,GROS,GROSSE-              
REMARK   3               : KUNSTLEVE,JIANG,KUSZEWSKI,NILGES, PANNU,             
REMARK   3               : READ,RICE,SIMONSON,WARREN                            
REMARK   3                                                                      
REMARK   3  REFINEMENT TARGET : NULL                                            
REMARK   3                                                                      
REMARK   3  DATA USED IN REFINEMENT.                                            
REMARK   3   RESOLUTION RANGE HIGH (ANGSTROMS) : 2.00                           
REMARK   3   RESOLUTION RANGE LOW  (ANGSTROMS) : 50.00                          
REMARK   3   DATA CUTOFF            (SIGMA(F)) : 2.000                          
REMARK   3   DATA CUTOFF HIGH         (ABS(F)) : 666370.390                     
REMARK   3   DATA CUTOFF LOW          (ABS(F)) : 0.0000                         
REMARK   3   COMPLETENESS (WORKING+TEST)   (%) : 80.0                           
REMARK   3   NUMBER OF REFLECTIONS             : 49150                          
REMARK   3                                                                      
REMARK   3  FIT TO DATA USED IN REFINEMENT.                                     
REMARK   3   CROSS-VALIDATION METHOD          : THROUGHOUT                      
REMARK   3   FREE R VALUE TEST SET SELECTION  : RANDOM                          
REMARK   3   R VALUE            (WORKING SET) : 0.172                           
REMARK   3   FREE R VALUE                     : 0.207                           
REMARK   3   FREE R VALUE TEST SET SIZE   (%) : 2.300                           
REMARK   3   FREE R VALUE TEST SET COUNT      : 1139                            
REMARK   3   ESTIMATED ERROR OF FREE R VALUE  : 0.005                           
REMARK   3                                                                      
REMARK   3  FIT IN THE HIGHEST RESOLUTION BIN.                                  
REMARK   3   TOTAL NUMBER OF BINS USED           : 6                            
REMARK   3   BIN RESOLUTION RANGE HIGH       (A) : 2.00                         
REMARK   3   BIN RESOLUTION RANGE LOW        (A) : 2.13                         
REMARK   3   BIN COMPLETENESS (WORKING+TEST) (%) : 57.70                        
REMARK   3   REFLECTIONS IN BIN    (WORKING SET) : 5706                         
REMARK   3   BIN R VALUE           (WORKING SET) : 0.2080                       
REMARK   3   BIN FREE R VALUE                    : 0.2530                       
REMARK   3   BIN FREE R VALUE TEST SET SIZE  (%) : 2.30                         
REMARK   3   BIN FREE R VALUE TEST SET COUNT     : 136                          
REMARK   3   ESTIMATED ERROR OF BIN FREE R VALUE : 0.017                        
REMARK   3                                                                      
REMARK   3  NUMBER OF NON-HYDROGEN ATOMS USED IN REFINEMENT.                    
REMARK   3   PROTEIN ATOMS            : 4900                                    
REMARK   3   NUCLEIC ACID ATOMS       : 0                                       
REMARK   3   HETEROGEN ATOMS          : 0                                       
REMARK   3   SOLVENT ATOMS            : 636                                     
REMARK   3                                                                      
REMARK   3  B VALUES.                                                           
REMARK   3   FROM WILSON PLOT           (A**2) : 23.50                          
REMARK   3   MEAN B VALUE      (OVERALL, A**2) : NULL                           
REMARK   3   OVERALL ANISOTROPIC B VALUE.                                       
REMARK   3    B11 (A**2) : -3.96000                                             
REMARK   3    B22 (A**2) : 5.52000                                              
REMARK   3    B33 (A**2) : -1.56000                                             
REMARK   3    B12 (A**2) : 0.00000                                              
REMARK   3    B13 (A**2) : -0.09000                                             
REMARK   3    B23 (A**2) : 0.00000                                              
REMARK   3                                                                      
REMARK   3  ESTIMATED COORDINATE ERROR.                                         
REMARK   3   ESD FROM LUZZATI PLOT        (A) : 0.19                            
REMARK   3   ESD FROM SIGMAA              (A) : 0.18                            
REMARK   3   LOW RESOLUTION CUTOFF        (A) : 5.00                            
REMARK   3                                                                      
REMARK   3  CROSS-VALIDATED ESTIMATED COORDINATE ERROR.                         
REMARK   3   ESD FROM C-V LUZZATI PLOT    (A) : 0.19                            
REMARK   3   ESD FROM C-V SIGMAA          (A) : 0.11                            
REMARK   3                                                                      
REMARK   3  RMS DEVIATIONS FROM IDEAL VALUES.                                   
REMARK   3   BOND LENGTHS                 (A) : 0.018                           
REMARK   3   BOND ANGLES            (DEGREES) : 1.90                            
REMARK   3   DIHEDRAL ANGLES        (DEGREES) : 26.50                           
REMARK   3   IMPROPER ANGLES        (DEGREES) : 1.22                            
REMARK   3                                                                      
REMARK   3  ISOTROPIC THERMAL MODEL : RESTRAINED                                
REMARK   3                                                                      
REMARK   3  ISOTROPIC THERMAL FACTOR RESTRAINTS.    RMS    SIGMA                
REMARK   3   MAIN-CHAIN BOND              (A**2) : 1.340 ; 1.500                
REMARK   3   MAIN-CHAIN ANGLE             (A**2) : 2.020 ; 2.000                
REMARK   3   SIDE-CHAIN BOND              (A**2) : 2.210 ; 2.000                
REMARK   3   SIDE-CHAIN ANGLE             (A**2) : 3.200 ; 2.500                
REMARK   3                                                                      
REMARK   3  BULK SOLVENT MODELING.                                              
REMARK   3   METHOD USED : FLAT MODEL                                           
REMARK   3   KSOL        : 0.35                                                 
REMARK   3   BSOL        : 52.94                                                
REMARK   3                                                                      
REMARK   3  NCS MODEL : NULL                                                    
REMARK   3                                                                      
REMARK   3  NCS RESTRAINTS.                         RMS   SIGMA/WEIGHT          
REMARK   3   GROUP  1  POSITIONAL            (A) : NULL  ; NULL                 
REMARK   3   GROUP  1  B-FACTOR           (A**2) : NULL  ; NULL                 
REMARK   3                                                                      
REMARK   3  PARAMETER FILE  1  : PROTEIN_REP.PARAM                              
REMARK   3  PARAMETER FILE  2  : ION.PARAM                                      
REMARK   3  PARAMETER FILE  3  : WATER_REP.PARAM                                
REMARK   3  PARAMETER FILE  4  : NULL                                           
REMARK   3  TOPOLOGY FILE  1   : PROTEIN.TOP                                    
REMARK   3  TOPOLOGY FILE  2   : ION.TOP                                        
REMARK   3  TOPOLOGY FILE  3   : WATER_REP.TOP                                  
REMARK   3  TOPOLOGY FILE  4   : NULL                                           
REMARK   3                                                                      
REMARK   3  OTHER REFINEMENT REMARKS: NULL                                      
REMARK   4                                                                      
REMARK   4 1FNS COMPLIES WITH FORMAT V. 3.0, 1-DEC-2006                         
REMARK   4                                                                      
REMARK   4 THIS IS THE REMEDIATED VERSION OF THIS PDB ENTRY.                    
REMARK   4 REMEDIATED DATA FILE REVISION 3.100 (2007-03-17)                     
REMARK 100                                                                      
REMARK 100 THIS ENTRY HAS BEEN PROCESSED BY RCSB .                              
REMARK 100 THE RCSB ID CODE IS RCSB011748.                                      
REMARK 200                                                                      
REMARK 200 EXPERIMENTAL DETAILS                                                 
REMARK 200  EXPERIMENT TYPE                : X-RAY DIFFRACTION                  
REMARK 200  DATE OF DATA COLLECTION        : NULL                               
REMARK 200  TEMPERATURE           (KELVIN) : 90.0                               
REMARK 200  PH                             : NULL                               
REMARK 200  NUMBER OF CRYSTALS USED        : 1                                  
REMARK 200                                                                      
REMARK 200  SYNCHROTRON              (Y/N) : Y                                  
REMARK 200  RADIATION SOURCE               : SSRL                               
REMARK 200  BEAMLINE                       : BL7-1                              
REMARK 200  X-RAY GENERATOR MODEL          : NULL                               
REMARK 200  MONOCHROMATIC OR LAUE    (M/L) : M                                  
REMARK 200  WAVELENGTH OR RANGE        (A) : NULL                               
REMARK 200  MONOCHROMATOR                  : NULL                               
REMARK 200  OPTICS                         : NULL                               
REMARK 200                                                                      
REMARK 200  DETECTOR TYPE                  : IMAGE PLATE                        
REMARK 200  DETECTOR MANUFACTURER          : MARRESEARCH                        
REMARK 200  INTENSITY-INTEGRATION SOFTWARE : NULL                               
REMARK 200  DATA SCALING SOFTWARE          : NULL                               
REMARK 200                                                                      
REMARK 200  NUMBER OF UNIQUE REFLECTIONS   : NULL                               
REMARK 200  RESOLUTION RANGE HIGH      (A) : NULL                               
REMARK 200  RESOLUTION RANGE LOW       (A) : NULL                               
REMARK 200  REJECTION CRITERIA  (SIGMA(I)) : NULL                               
REMARK 200                                                                      
REMARK 200 OVERALL.                                                             
REMARK 200  COMPLETENESS FOR RANGE     (%) : NULL                               
REMARK 200  DATA REDUNDANCY                : NULL                               
REMARK 200  R MERGE                    (I) : NULL                               
REMARK 200  R SYM                      (I) : NULL                               
REMARK 200   FOR THE DATA SET  : NULL                               
REMARK 200                                                                      
REMARK 200 IN THE HIGHEST RESOLUTION SHELL.                                     
REMARK 200  HIGHEST RESOLUTION SHELL, RANGE HIGH (A) : NULL                     
REMARK 200  HIGHEST RESOLUTION SHELL, RANGE LOW  (A) : NULL                     
REMARK 200  COMPLETENESS FOR SHELL     (%) : NULL                               
REMARK 200  DATA REDUNDANCY IN SHELL       : NULL                               
REMARK 200  R MERGE FOR SHELL          (I) : NULL                               
REMARK 200  R SYM FOR SHELL            (I) : NULL                               
REMARK 200   FOR SHELL         : NULL                               
REMARK 200                                                                      
REMARK 200 DIFFRACTION PROTOCOL: SINGLE WAVELENGTH                              
REMARK 200 METHOD USED TO DETERMINE THE STRUCTURE: NULL                         
REMARK 200 SOFTWARE USED: NULL                                                  
REMARK 200 STARTING MODEL: NULL                                                 
REMARK 200                                                                      
REMARK 200 REMARK: NULL                                                         
REMARK 280                                                                      
REMARK 280 CRYSTAL                                                              
REMARK 280 SOLVENT CONTENT, VS   (%): 62.27                                     
REMARK 280 MATTHEWS COEFFICIENT, VM (ANGSTROMS**3/DA): 3.26                     
REMARK 280                                                                      
REMARK 280 CRYSTALLIZATION CONDITIONS: NULL                                     
REMARK 290                                                                      
REMARK 290 CRYSTALLOGRAPHIC SYMMETRY                                            
REMARK 290 SYMMETRY OPERATORS FOR SPACE GROUP: C 1 2 1                          
REMARK 290                                                                      
REMARK 290      SYMOP   SYMMETRY                                                
REMARK 290     NNNMMM   OPERATOR                                                
REMARK 290       1555   X,Y,Z                                                   
REMARK 290       2555   -X,Y,-Z                                                 
REMARK 290       3555   1/2+X,1/2+Y,Z                                           
REMARK 290       4555   1/2-X,1/2+Y,-Z                                          
REMARK 290                                                                      
REMARK 290     WHERE NNN -> OPERATOR NUMBER                                     
REMARK 290           MMM -> TRANSLATION VECTOR                                  
REMARK 290                                                                      
REMARK 290 CRYSTALLOGRAPHIC SYMMETRY TRANSFORMATIONS                            
REMARK 290 THE FOLLOWING TRANSFORMATIONS OPERATE ON THE ATOM/HETATM             
REMARK 290 RECORDS IN THIS ENTRY TO PRODUCE CRYSTALLOGRAPHICALLY                
REMARK 290 RELATED MOLECULES.                                                   
REMARK 290   SMTRY1   1  1.000000  0.000000  0.000000        0.00000            
REMARK 290   SMTRY2   1  0.000000  1.000000  0.000000        0.00000            
REMARK 290   SMTRY3   1  0.000000  0.000000  1.000000        0.00000            
REMARK 290   SMTRY1   2 -1.000000  0.000000  0.000000        0.00000            
REMARK 290   SMTRY2   2  0.000000  1.000000  0.000000        0.00000            
REMARK 290   SMTRY3   2  0.000000  0.000000 -1.000000        0.00000            
REMARK 290   SMTRY1   3  1.000000  0.000000  0.000000      104.69800            
REMARK 290   SMTRY2   3  0.000000  1.000000  0.000000       31.33650            
REMARK 290   SMTRY3   3  0.000000  0.000000  1.000000        0.00000            
REMARK 290   SMTRY1   4 -1.000000  0.000000  0.000000      104.69800            
REMARK 290   SMTRY2   4  0.000000  1.000000  0.000000       31.33650            
REMARK 290   SMTRY3   4  0.000000  0.000000 -1.000000        0.00000            
REMARK 290                                                                      
REMARK 290 REMARK: NULL                                                         
REMARK 300                                                                      
REMARK 300 BIOMOLECULE: 1                                                       
REMARK 300 THIS ENTRY CONTAINS THE CRYSTALLOGRAPHIC ASYMMETRIC UNIT             
REMARK 300 WHICH CONSISTS OF 3 CHAIN(S). SEE REMARK 350 FOR                     
REMARK 300 INFORMATION ON GENERATING THE BIOLOGICAL MOLECULE(S).                
REMARK 350                                                                      
REMARK 350 GENERATING THE BIOMOLECULE                                           
REMARK 350 COORDINATES FOR A COMPLETE MULTIMER REPRESENTING THE KNOWN           
REMARK 350 BIOLOGICALLY SIGNIFICANT OLIGOMERIZATION STATE OF THE                
REMARK 350 MOLECULE CAN BE GENERATED BY APPLYING BIOMT TRANSFORMATIONS          
REMARK 350 GIVEN BELOW.  BOTH NON-CRYSTALLOGRAPHIC AND                          
REMARK 350 CRYSTALLOGRAPHIC OPERATIONS ARE GIVEN.                               
REMARK 350                                                                      
REMARK 350 BIOMOLECULE: 1                                                       
REMARK 350 APPLY THE FOLLOWING TO CHAINS: L, H, A                               
REMARK 350   BIOMT1   1  1.000000  0.000000  0.000000        0.00000            
REMARK 350   BIOMT2   1  0.000000  1.000000  0.000000        0.00000            
REMARK 350   BIOMT3   1  0.000000  0.000000  1.000000        0.00000            
REMARK 375                                                                      
REMARK 375 SPECIAL POSITION                                                     
REMARK 375 THE FOLLOWING ATOMS ARE FOUND TO BE WITHIN 0.15 ANGSTROMS            
REMARK 375 OF A SYMMETRY RELATED ATOM AND ARE ASSUMED TO BE ON SPECIAL          
REMARK 375 POSITIONS.                                                           
REMARK 375                                                                      
REMARK 375 ATOM RES CSSEQI                                                      
REMARK 375      HOH  1226   LIES ON A SPECIAL POSITION.                         
REMARK 465                                                                      
REMARK 465 MISSING RESIDUES                                                     
REMARK 465 THE FOLLOWING RESIDUES WERE NOT LOCATED IN THE                       
REMARK 465 EXPERIMENT. (M=MODEL NUMBER; RES=RESIDUE NAME; C=CHAIN               
REMARK 465 IDENTIFIER; SSSEQ=SEQUENCE NUMBER; I=INSERTION CODE.)                
REMARK 465                                                                      
REMARK 465   M RES C SSSEQI                                                     
REMARK 465     ALA H   352                                                      
REMARK 465     ALA H   353                                                      
REMARK 465     GLN H   354                                                      
REMARK 465     THR H   355                                                      
REMARK 465     ASN H   356                                                      
REMARK 500                                                                      
REMARK 500 GEOMETRY AND STEREOCHEMISTRY                                         
REMARK 500 SUBTOPIC: COVALENT BOND LENGTHS                                      
REMARK 500                                                                      
REMARK 500 THE STEREOCHEMICAL PARAMETERS OF THE FOLLOWING RESIDUES              
REMARK 500 HAVE VALUES WHICH DEVIATE FROM EXPECTED VALUES BY MORE               
REMARK 500 THAN 6*RMSD (M=MODEL NUMBER; RES=RESIDUE NAME; C=CHAIN               
REMARK 500 IDENTIFIER; SSEQ=SEQUENCE NUMBER; I=INSERTION CODE).                 
REMARK 500                                                                      
REMARK 500 STANDARD TABLE:                                                      
REMARK 500 FORMAT: (10X,I3,1X,2(A3,1X,A1,I4,A1,1X,A4,3X),F6.3)                  
REMARK 500                                                                      
REMARK 500 EXPECTED VALUES: ENGH AND HUBER, 1991                                
REMARK 500                                                                      
REMARK 500  M RES CSSEQI ATM1   RES CSSEQI ATM2   DEVIATION                     
REMARK 500    MET A 540   SD    MET A 540   CE     0.115                        
REMARK 500                                                                      
REMARK 500 GEOMETRY AND STEREOCHEMISTRY                                         
REMARK 500 SUBTOPIC: COVALENT BOND ANGLES                                       
REMARK 500                                                                      
REMARK 500 THE STEREOCHEMICAL PARAMETERS OF THE FOLLOWING RESIDUES              
REMARK 500 HAVE VALUES WHICH DEVIATE FROM EXPECTED VALUES BY MORE               
REMARK 500 THAN 6*RMSD (M=MODEL NUMBER; RES=RESIDUE NAME; C=CHAIN               
REMARK 500 IDENTIFIER; SSEQ=SEQUENCE NUMBER; I=INSERTION CODE).                 
REMARK 500                                                                      
REMARK 500 STANDARD TABLE:                                                      
REMARK 500 FORMAT: (10X,I3,1X,A3,1X,A1,I4,A1,3(1X,A4,2X),12X,F5.1)              
REMARK 500                                                                      
REMARK 500 EXPECTED VALUES: ENGH AND HUBER, 1991                                
REMARK 500                                                                      
REMARK 500  M RES CSSEQI ATM1   ATM2   ATM3                                     
REMARK 500    LEU L  33   CA  -  CB  -  CG  ANGL. DEV. =-17.7 DEGREES           
REMARK 500    LEU L 136   N   -  CA  -  C   ANGL. DEV. =-11.8 DEGREES           
REMARK 500    CYS L 214   N   -  CA  -  C   ANGL. DEV. =-18.0 DEGREES           
REMARK 500    GLY H 439   N   -  CA  -  C   ANGL. DEV. = 13.7 DEGREES           
REMARK 500    ASP A 560   N   -  CA  -  C   ANGL. DEV. =-14.6 DEGREES           
REMARK 500    GLY A 561   N   -  CA  -  C   ANGL. DEV. =-11.5 DEGREES           
REMARK 500    ALA A 592   N   -  CA  -  C   ANGL. DEV. =-14.5 DEGREES           
REMARK 500                                                                      
REMARK 500 GEOMETRY AND STEREOCHEMISTRY                                         
REMARK 500 SUBTOPIC: TORSION ANGLES                                             
REMARK 500                                                                      
REMARK 500 TORSION ANGLES OUTSIDE THE EXPECTED RAMACHANDRAN REGIONS:            
REMARK 500 (M=MODEL NUMBER; RES=RESIDUE NAME; C=CHAIN IDENTIFIER;               
REMARK 500 SSEQ=SEQUENCE NUMBER; I=INSERTION CODE).                             
REMARK 500                                                                      
REMARK 500 STANDARD TABLE:                                                      
REMARK 500 FORMAT:(10X,I3,1X,A3,1X,A1,I4,A1,4X,F7.2,3X,F7.2)                    
REMARK 500                                                                      
REMARK 500  M RES CSSEQI        PSI       PHI                                   
REMARK 500    THR L  51      -44.86     63.94                                   
REMARK 525                                                                      
REMARK 525 SOLVENT                                                              
REMARK 525 THE FOLLOWING SOLVENT MOLECULES LIE FARTHER THAN EXPECTED            
REMARK 525 FROM THE PROTEIN OR NUCLEIC ACID MOLECULE AND MAY BE                 
REMARK 525 ASSOCIATED WITH A SYMMETRY RELATED MOLECULE (M=MODEL                 
REMARK 525 NUMBER; RES=RESIDUE NAME; C=CHAIN IDENTIFIER; SSEQ=SEQUENCE          
REMARK 525 NUMBER; I=INSERTION CODE):                                           
REMARK 525                                                                      
REMARK 525  M RES CSSEQI                                                        
REMARK 525    HOH  1164        DISTANCE =  5.39 ANGSTROMS                       
DBREF  1FNS A  508   702  UNP    P04275   VWF_HUMAN     1271   1465             
SEQADV 1FNS MET A  507  UNP  P04275              CLONING ARTIFACT               
SEQADV 1FNS VAL A  546  UNP  P04275    ILE  1309 CONFLICT                       
SEQRES   1 L  214  ASP ILE GLN MET THR GLN SER PRO SER SER LEU SER ALA          
SEQRES   2 L  214  SER LEU GLY ASP ARG VAL THR ILE SER CYS SER ALA SER          
SEQRES   3 L  214  GLN ASP ILE ASN LYS TYR LEU ASN TRP TYR GLN GLN LYS          
SEQRES   4 L  214  PRO ASP GLY ALA VAL LYS LEU LEU ILE PHE TYR THR SER          
SEQRES   5 L  214  SER LEU HIS SER GLY VAL PRO SER ARG PHE SER GLY SER          
SEQRES   6 L  214  GLY SER GLY THR ASP TYR SER LEU THR ILE SER ASN LEU          
SEQRES   7 L  214  GLU PRO GLU ASP ILE ALA THR TYR TYR CYS GLN GLN TYR          
SEQRES   8 L  214  GLU LYS LEU PRO TRP THR PHE GLY GLY GLY THR LYS LEU          
SEQRES   9 L  214  GLU VAL LYS ARG ALA ASP ALA ALA PRO THR VAL SER ILE          
SEQRES  10 L  214  PHE PRO PRO SER SER GLU GLN LEU THR SER GLY GLY ALA          
SEQRES  11 L  214  SER VAL VAL CYS PHE LEU ASN ASN PHE TYR PRO LYS ASP          
SEQRES  12 L  214  ILE ASN VAL LYS TRP LYS ILE ASP GLY SER GLU ARG GLN          
SEQRES  13 L  214  ASN GLY VAL LEU ASN SER TRP THR ASP GLN ASP SER LYS          
SEQRES  14 L  214  ASP SER THR TYR SER MET SER SER THR LEU THR LEU THR          
SEQRES  15 L  214  LYS ASP GLU TYR GLU ARG HIS ASN SER TYR THR CYS GLU          
SEQRES  16 L  214  ALA THR HIS LYS THR SER THR SER PRO ILE VAL LYS SER          
SEQRES  17 L  214  PHE ASN ARG ASN GLU CYS                                      
SEQRES   1 H  225  GLN VAL GLN LEU LYS GLU SER GLY PRO GLY LEU VAL ALA          
SEQRES   2 H  225  PRO SER GLN SER LEU SER ILE THR CYS THR VAL SER GLY          
SEQRES   3 H  225  PHE SER LEU THR ASP TYR GLY VAL ASP TRP VAL ARG GLN          
SEQRES   4 H  225  PRO PRO GLY LYS GLY LEU GLU TRP LEU GLY MET ILE TRP          
SEQRES   5 H  225  GLY ASP GLY SER THR ASP TYR ASN SER ALA LEU LYS SER          
SEQRES   6 H  225  ARG LEU SER ILE THR LYS ASP ASN SER LYS SER GLN VAL          
SEQRES   7 H  225  PHE LEU LYS MET ASN SER LEU GLN THR ASP ASP THR ALA          
SEQRES   8 H  225  ARG TYR TYR CYS VAL ARG ASP PRO ALA ASP TYR GLY ASN          
SEQRES   9 H  225  TYR ASP TYR ALA LEU ASP TYR TRP GLY GLN GLY THR SER          
SEQRES  10 H  225  VAL THR VAL SER SER ALA LYS THR THR PRO PRO SER VAL          
SEQRES  11 H  225  TYR PRO LEU ALA PRO GLY SER ALA ALA GLN THR ASN SER          
SEQRES  12 H  225  MET VAL THR LEU GLY CYS LEU VAL LYS GLY TYR PHE PRO          
SEQRES  13 H  225  GLU PRO VAL THR VAL THR TRP ASN SER GLY SER LEU SER          
SEQRES  14 H  225  SER GLY VAL HIS THR PHE PRO ALA VAL LEU GLN SER ASP          
SEQRES  15 H  225  LEU TYR THR LEU SER SER SER VAL THR VAL PRO SER SER          
SEQRES  16 H  225  THR TRP PRO SER GLU THR VAL THR CYS ASN VAL ALA HIS          
SEQRES  17 H  225  PRO ALA SER SER THR LYS VAL ASP LYS LYS ILE VAL PRO          
SEQRES  18 H  225  ARG ASP CYS GLY                                              
SEQRES   1 A  196  MET TYR CYS SER ARG LEU LEU ASP LEU VAL PHE LEU LEU          
SEQRES   2 A  196  ASP GLY SER SER ARG LEU SER GLU ALA GLU PHE GLU VAL          
SEQRES   3 A  196  LEU LYS ALA PHE VAL VAL ASP MET MET GLU ARG LEU ARG          
SEQRES   4 A  196  VAL SER GLN LYS TRP VAL ARG VAL ALA VAL VAL GLU TYR          
SEQRES   5 A  196  HIS ASP GLY SER HIS ALA TYR ILE GLY LEU LYS ASP ARG          
SEQRES   6 A  196  LYS ARG PRO SER GLU LEU ARG ARG ILE ALA SER GLN VAL          
SEQRES   7 A  196  LYS TYR ALA GLY SER GLN VAL ALA SER THR SER GLU VAL          
SEQRES   8 A  196  LEU LYS TYR THR LEU PHE GLN ILE PHE SER LYS ILE ASP          
SEQRES   9 A  196  ARG PRO GLU ALA SER ARG ILE ALA LEU LEU LEU MET ALA          
SEQRES  10 A  196  SER GLN GLU PRO GLN ARG MET SER ARG ASN PHE VAL ARG          
SEQRES  11 A  196  TYR VAL GLN GLY LEU LYS LYS LYS LYS VAL ILE VAL ILE          
SEQRES  12 A  196  PRO VAL GLY ILE GLY PRO HIS ALA ASN LEU LYS GLN ILE          
SEQRES  13 A  196  ARG LEU ILE GLU LYS GLN ALA PRO GLU ASN LYS ALA PHE          
SEQRES  14 A  196  VAL LEU SER SER VAL ASP GLU LEU GLU GLN GLN ARG ASP          
SEQRES  15 A  196  GLU ILE VAL SER TYR LEU CYS ASP LEU ALA PRO GLU ALA          
SEQRES  16 A  196  PRO                                                          
FORMUL   4  HOH   *636(H2 O)                                                    
HELIX    1   1 GLU L   79  ILE L   83  5                                   5    
HELIX    2   2 SER L  121  THR L  126  1                                   6    
HELIX    3   3 LYS L  183  GLU L  187  1                                   5    
HELIX    4   4 SER H  275  LYS H  278  5                                   4    
HELIX    5   5 ASN H  287  LYS H  289  5                                   3    
HELIX    6   6 GLN H  300  THR H  304  5                                   5    
HELIX    7   7 TYR H  316  TYR H  319  5                                   4    
HELIX    8   8 SER H  379  SER H  381  5                                   3    
HELIX    9   9 SER H  409  TRP H  411  5                                   3    
HELIX   10  10 PRO H  423  SER H  426  5                                   4    
HELIX   11  11 SER A  526  ARG A  543  1                                  18    
HELIX   12  12 ARG A  573  GLN A  583  1                                  11    
HELIX   13  13 SER A  593  GLN A  604  1                                  12    
HELIX   14  14 PRO A  627  ARG A  632  5                                   6    
HELIX   15  15 ASN A  633  LYS A  644  1                                  12    
HELIX   16  16 ASN A  658  ALA A  669  1                                  12    
HELIX   17  17 ASP A  681  LEU A  697  1                                  17    
SHEET    1   A 4 MET L   4  THR L   5  0                                        
SHEET    2   A 4 VAL L  19  ALA L  25 -1  O  SER L  24   N  THR L   5           
SHEET    3   A 4 ASP L  70  ILE L  75 -1  N  TYR L  71   O  CYS L  23           
SHEET    4   A 4 PHE L  62  SER L  67 -1  O  SER L  63   N  THR L  74           
SHEET    1   B 5 SER L  53  LEU L  54  0                                        
SHEET    2   B 5 VAL L  44  PHE L  49 -1  O  PHE L  49   N  SER L  53           
SHEET    3   B 5 LEU L  33  GLN L  38 -1  O  TRP L  35   N  LEU L  47           
SHEET    4   B 5 THR L  85  GLN L  90 -1  O  THR L  85   N  GLN L  38           
SHEET    5   B 5 THR L  97  PHE L  98 -1  O  THR L  97   N  GLN L  90           
SHEET    1   C 6 SER L  53  LEU L  54  0                                        
SHEET    2   C 6 VAL L  44  PHE L  49 -1  O  PHE L  49   N  SER L  53           
SHEET    3   C 6 LEU L  33  GLN L  38 -1  O  TRP L  35   N  LEU L  47           
SHEET    4   C 6 THR L  85  GLN L  90 -1  O  THR L  85   N  GLN L  38           
SHEET    5   C 6 THR L 102  VAL L 106 -1  O  THR L 102   N  TYR L  86           
SHEET    6   C 6 SER L  10  ALA L  13  1  N  LEU L  11   O  LYS L 103           
SHEET    1   D 4 THR L 114  PHE L 118  0                                        
SHEET    2   D 4 GLY L 129  PHE L 139 -1  O  VAL L 133   N  PHE L 118           
SHEET    3   D 4 TYR L 173  THR L 182 -1  O  TYR L 173   N  PHE L 139           
SHEET    4   D 4 VAL L 159  TRP L 163 -1  N  LEU L 160   O  THR L 178           
SHEET    1   E 4 SER L 153  ARG L 155  0                                        
SHEET    2   E 4 ASN L 145  ILE L 150 -1  O  TRP L 148   N  ARG L 155           
SHEET    3   E 4 SER L 191  THR L 197 -1  N  THR L 193   O  LYS L 149           
SHEET    4   E 4 ILE L 205  ASN L 210 -1  O  ILE L 205   N  ALA L 196           
SHEET    1   F 4 GLN H 217  SER H 221  0                                        
SHEET    2   F 4 LEU H 232  SER H 239 -1  N  THR H 235   O  SER H 221           
SHEET    3   F 4 GLN H 291  MET H 296 -1  O  VAL H 292   N  CYS H 236           
SHEET    4   F 4 LEU H 281  ASP H 286 -1  N  SER H 282   O  LYS H 295           
SHEET    1   G 5 THR H 271  TYR H 273  0                                        
SHEET    2   G 5 GLU H 260  ILE H 265 -1  N  MET H 264   O  ASP H 272           
SHEET    3   G 5 GLY H 247  GLN H 253 -1  N  VAL H 248   O  ILE H 265           
SHEET    4   G 5 ALA H 305  ASP H 312 -1  O  ARG H 306   N  GLN H 253           
SHEET    5   G 5 TYR H 325  TRP H 326 -1  O  TYR H 325   N  ARG H 311           
SHEET    1   H 6 THR H 271  TYR H 273  0                                        
SHEET    2   H 6 GLU H 260  ILE H 265 -1  N  MET H 264   O  ASP H 272           
SHEET    3   H 6 GLY H 247  GLN H 253 -1  N  VAL H 248   O  ILE H 265           
SHEET    4   H 6 ALA H 305  ASP H 312 -1  O  ARG H 306   N  GLN H 253           
SHEET    5   H 6 THR H 330  VAL H 334 -1  O  THR H 330   N  TYR H 307           
SHEET    6   H 6 LEU H 225  VAL H 226  1  N  VAL H 226   O  THR H 333           
SHEET    1   I 4 SER H 343  LEU H 347  0                                        
SHEET    2   I 4 MET H 358  TYR H 368 -1  O  GLY H 362   N  LEU H 347           
SHEET    3   I 4 TYR H 398  PRO H 407 -1  N  TYR H 398   O  TYR H 368           
SHEET    4   I 4 VAL H 386  THR H 388 -1  O  HIS H 387   N  SER H 403           
SHEET    1   J 4 SER H 343  LEU H 347  0                                        
SHEET    2   J 4 MET H 358  TYR H 368 -1  O  GLY H 362   N  LEU H 347           
SHEET    3   J 4 TYR H 398  PRO H 407 -1  N  TYR H 398   O  TYR H 368           
SHEET    4   J 4 VAL H 392  LEU H 393 -1  N  VAL H 392   O  THR H 399           
SHEET    1   K 3 THR H 374  TRP H 377  0                                        
SHEET    2   K 3 THR H 417  HIS H 422 -1  N  ASN H 419   O  THR H 376           
SHEET    3   K 3 THR H 427  LYS H 432 -1  O  THR H 427   N  HIS H 422           
SHEET    1   L 6 SER A 562  ILE A 566  0                                        
SHEET    2   L 6 VAL A 551  TYR A 558 -1  O  VAL A 555   N  TYR A 565           
SHEET    3   L 6 LEU A 513  ASP A 520  1  O  LEU A 513   N  ARG A 552           
SHEET    4   L 6 SER A 615  MET A 622  1  O  SER A 615   N  ASP A 514           
SHEET    5   L 6 VAL A 646  ILE A 653  1  O  ILE A 647   N  ALA A 618           
SHEET    6   L 6 PHE A 675  LEU A 677  1  N  PHE A 675   O  PRO A 650           
SSBOND   1 CYS L   23    CYS L   88                                             
SSBOND   2 CYS L  134    CYS L  194                                             
SSBOND   3 CYS L  214    CYS H  438                                             
SSBOND   4 CYS H  236    CYS H  309                                             
SSBOND   5 CYS H  363    CYS H  418                                             
SSBOND   6 CYS A  509    CYS A  695                                             
CISPEP   1 LEU L   94    PRO L   95          0        -0.62                     
CISPEP   2 TYR L  140    PRO L  141          0         0.44                     
CISPEP   3 PHE H  369    PRO H  370          0         0.09                     
CISPEP   4 GLU H  371    PRO H  372          0        -0.66                     
CISPEP   5 TRP H  411    PRO H  412          0         0.48                     
CRYST1  209.396   62.673   73.789  90.00 108.88  90.00 C 1 2 1       4          
ORIGX1      1.000000  0.000000  0.000000        0.00000                         
ORIGX2      0.000000  1.000000  0.000000        0.00000                         
ORIGX3      0.000000  0.000000  1.000000        0.00000                         
SCALE1      0.004776  0.000000  0.001633        0.00000                         
SCALE2      0.000000  0.015956  0.000000        0.00000                         
SCALE3      0.000000  0.000000  0.014323        0.00000